PayYourBillMyChildren'sPatientPortalInternationalVisitorsWaystoHelpCareersDonateDonateForPatientsForHealthCareProfessionalsPrograms&ServicesConditions&TreatmentsResearchInnovationCloseForPatientsForHealthCareProfessionalsPrograms&ServicesConditions&TreatmentsResearchInnovationInternationalVisitorsWaystoHelpCareersDonateDonatePayYourBillMyChildren'sPatientPortalConditionsContacttheCenterforChildhoodLiverDisease617-355-5837RequestanAppointmentRequestASecondOpinionContacttheCenterforChildhoodLiverDisease617-355-5837RequestanAppointmentRequestASecondOpinionNavigationOverviewDiagnosis&TreatmentsPrograms&ServicesCholedochalCystsWhatisacholedochalcyst?Acholedochalcystisacongenitalanomalyoftheduct(tube)thattransportsbilefromthelivertothegallbladderandsmallintestine.Theliverproducesbiletohelpdigestfood.Whenachildhasacholedochalcyst,aswellingofthatduct,bilemaybackupintheliver.Thiscancauseliverproblemsorinflammationofthepancreas(pancreatitis)becauseitblocksthemainductfromthepancreasglandtotheintestine.Childrenwithcholedochalcystshaveahigherrateofcancerofthebileductinadulthood.Earlytreatmentcanreducetheserisks.Choledochalcystsarerare:oneinevery100,000to150,000childreninWesterncountriesisbornwithcholedochalcysts.Girlsarefourtimesmorelikelytobeaffectedthanboys.TheconditionismorecommoninEastAsiancountries,especiallyJapan,thoughresearchersdonotknowwhy.Choledochalcystsarecongenital.Whatarethesymptomsofacholedochalcyst?Althoughchildrenarebornwithcholedochalcysts,symptomsmayappearininfancyornotforseveralyears.Thefollowingsymptomsmayoccurininfantsorolderchildren:abdominalmasspainintherightupperbellyjaundicenauseaandvomitingfeverWhatcausescholedochalcysts?Thebileducttransportsbilefromtheliver,throughthepancreas,tothefirstpartofthesmallintestine(theduodenum).Researchersbelievethatcholedochalcystsformwhenthereisanabnormalityattheintersectionbetweenthebileductandpancreaticduct.Thisabnormalconnectionforcespancreaticjuicetoflowbackwardintothebileductandmaycausecyststoform.Typesandlocations

Choledochal cysts represent congenital cystic dilatations of the biliary tree. Diagnosis relies on the exclusion of other conditions (e.g. tumor, gallstone, ...×ArticlesLogInCasesSignUpCoursesQuizBlogDonateAbout×MenuSearchADVERTISEMENT:Radiopaediaisfreethankstooursupportersandadvertisers.BecomeaGoldSupporterandseenoads.ArticlesCasesCoursesLogInLoginSignup{"url":"/signup-modal-props.json?lang=us\u0026email="}ArticlesCasesCoursesQuizAboutBlogGoad-freeSearchCholedochalcystDrAnujAggarwalandAssocProfFrankGaillard◉◈etal.Choledochalcystsrepresentcongenitalcysticdilatationsofthebiliarytree.Diagnosisreliesontheexclusionofotherconditions(e.g.tumor, gallstone, inflammation) asacauseofbiliaryductdilatation.Onthispage:Article:EpidemiologyClinicalpresentationPathologyRadiographicfeaturesTreatmentandprognosisDifferentialdiagnosisSeealsoReferencesImages:CasesandfiguresEpidemiologyCholedochalcystsarerare,withanincidenceof1:100,000-150,000.Althoughtheymaybediscoveredatanyage,60%arediagnosedbeforetheageof10years1. ThereisastrongfemalepredilectionwithM:Fratioof1:4.ThereisagreaterprevalenceinEastAsia.ClinicalpresentationClassicalpresentationincludesthetriadof1:abdominalpainjaundiceabdominalmassThistriadishoweveronlypresentin~40%(range19-60%)ofcases,withpalpablemassbeingtheleastcommonmanifestation.PathologyTheiretiologyisuncertain,butacloseassociationwiththeanomalousformationofthepancreaticobiliaryductaljunctionisreportedinsomesubtypes1.Duetothisanomaly,thereisalargecommonchanneldrainingpancreaticandbileduct.Thusthepancreaticjuicescausecholangitisandbileductwalldestruction,whichtogetherwithdistalstenosisduetoscarringresultintheformationofacholedochalcyst.AssociationsAnumberofassociationsarerecognized,including1:biliaryatresiahepaticfibrosisassociatedwithtypeV(Carolidisease)ClassificationCommonlyacceptedclassificationcurrentlyisonedevisedbyTodanietal.Therearefivemaintypes,withseveralsubtypessomeofwhichcanbepathologicallyunrelated:typeI: mostcommon,accountingfor80-90% 1(thistypecanpresenti

PayYourBillMyChildren'sPatientPortalInternationalVisitorsWaystoHelpCareersDonateDonateForPatientsForHealthCareProfessionalsPrograms&ServicesConditions&TreatmentsResearchInnovationCloseForPatientsForHealthCareProfessionalsPrograms&ServicesConditions&TreatmentsResearchInnovationInternationalVisitorsWaystoHelpCareersDonateDonatePayYourBillMyChildren'sPatientPortalConditionsContacttheCenterforChildhoodLiverDisease617-355-5837RequestanAppointmentRequestASecondOpinionContacttheCenterforChildhoodLiverDisease617-355-5837RequestanAppointmentRequestASecondOpinionNavigationOverviewDiagnosis&TreatmentsPrograms&ServicesCholedochalCysts|Diagnosis&Treatments Howarecholedochalcystsdiagnosed?Somecholedochalcystsaredetectedonanultrasound beforeachildisborn.Sometimesafterababyisborn,thechild'sparentordoctormaynoticeamassintheupperrightabdomen.Acombinationoftestshelpdoctorsverifythatachildhascholedochalcysts:Computerizedtomographyscan(CTorCATscan)—ACTscanshowsdetailedimagesofanypartofthebiliarysystem.Cholangiography— aradiographicvisualizationofachild’sbileductHowarecholedochalcyststreated?Childrenwithcholedochalcystsneedsurgerytoremovethem.Thisinvolvesremovingalobeoftheliverifthecystsareintrahepatic,orpartoftheductoutsideoftheliverifthecystsarelocatedthere.Thissurgeryalsoincludesbiliaryreconstructionusingapieceofintestine.MinimallyinvasivesurgerySurgeonareoftenabletoremovecholedochalcystswithaminimallyinvasivesurgerycalledalaparoscopy.Withthistechnique,smallinstrumentsguidedbyasmalltelescopearepassedthroughthebody.Inmanycaseschildren,cangohomeinonetotwodaysandreturntotheirnormalactivitiesmorequicklythanchildrenwhohaveopensurgery.Otherbenefitsofminimallyinvasivesurgeryinclude:verysmallscars,whicharedifficulttoseeafterseveralmonthslesspainaftersurgeryusuallyashorterhospitalstayWithoutsurgery,childrenwithcholedochalcystshaveanongoingriskofotherproblems:biliaryobstructioninfectionoftheductsjaundicecirrhosisInadulthood,choledochalcystscanbecomecancerousifleftuntreated. Thecommitmentandco

and subsequent dilatation. Choledochal cysts appear as cystic or fusiform di- ... bile duct, also known as a choledochal cyst, is an un- common but serious.

×ArticlesLogInCasesSignUpCoursesQuizBlogDonateAbout×MenuSearchADVERTISEMENT:Radiopaediaisfreethankstooursupportersandadvertisers.BecomeaGoldSupporterandseenoads.ArticlesCasesCoursesLogInLoginSignup{"url":"/signup-modal-props.json?lang=us\u0026email="}ArticlesCasesCoursesQuizAboutBlogGoad-freeSearchTodaniclassificationofbileductcystsDrYahyaBaba◉andRadswiki◉etal.TheTodaniclassificationofbileductcystsdividescholedochalcysts intofivegroups.Onthispage:Article:ClassificationHistoryandetymologySeealsoReferencesImages:CasesandfiguresClassificationTypeISee:typeIcholedochalcystaccountfor80-90%ofallbileductcystscharacterizedbyfusiformdilationoftheextrahepaticbileductasubclassificationhasbeenproposedIa:dilatationofextrahepaticbileduct(entire)Ib:dilatationofextrahepaticbileduct(focalsegment)Ic:dilatationofthecommonbileductportionofextrahepaticbileductTheorizedtoformastheresultofrefluxofpancreaticsecretionsintothebileductviaananomalouspancreaticobiliaryjunction.Somebelievethemtoarisefromductalplateanomalies.TypeIIAlsoknownasabileductdiverticulum. Accountfor3%ofallbileductcysts. Saccularoutpouchings,representingatruediverticulum, arisingfromthesupraduodenalextrahepaticbileductortheintrahepaticbileducts. TypeIIIAlsoknownasacholedochocele:accountfor5%ofallbileductcystsrepresentprotrusionofafocallydilated,intramuralsegmentofthedistalcommonbileductintotheduodenumCholedochocelesmaybesuccessfullymanagedwithendoscopicsphincterotomy,surgicalexcision,orboth,insymptomaticpatients.TypeIVMultiplecommunicatingintra-andextrahepaticductcysts:secondmostcommontypeofbileductcysts(10%)subdividedintosubtypes:type4a:fusiformdilationoftheentireextrahepaticbileductwithextensionofdilationoftheintrahepaticbileductstype4b:multiplecysticdilationsinvolvingonlytheextrahepaticbileductTypeVAlsoknownasCarolidisease,whichisarareformofcongenitalbiliarycysticdiseasemanifestedbycysticdilationsofintrahepaticbileducts. Associationwithbenignrenaltubularectasiaandotherformsofrenalcysticdisease.HistoryandetymologyTheToda

Choledochal cysts appear as cystic or fusiform dilatation of the common bile duct at radiography. Ultrasonography is the best initial method of ...

×ArticlesLogInCasesSignUpCoursesQuizBlogDonateAbout×MenuSearchADVERTISEMENT:Radiopaediaisfreethankstooursupportersandadvertisers.BecomeaGoldSupporterandseenoads.ArticlesCasesCoursesLogInLoginSignup{"url":"/signup-modal-props.json?lang=us\u0026email="}ArticlesCasesCoursesQuizAboutBlogGoad-freeSearchTodaniclassificationofbileductcystsDrYahyaBaba◉andRadswiki◉etal.TheTodaniclassificationofbileductcystsdividescholedochalcysts intofivegroups.Onthispage:Article:ClassificationHistoryandetymologySeealsoReferencesImages:CasesandfiguresClassificationTypeISee:typeIcholedochalcystaccountfor80-90%ofallbileductcystscharacterizedbyfusiformdilationoftheextrahepaticbileductasubclassificationhasbeenproposedIa:dilatationofextrahepaticbileduct(entire)Ib:dilatationofextrahepaticbileduct(focalsegment)Ic:dilatationofthecommonbileductportionofextrahepaticbileductTheorizedtoformastheresultofrefluxofpancreaticsecretionsintothebileductviaananomalouspancreaticobiliaryjunction.Somebelievethemtoarisefromductalplateanomalies.TypeIIAlsoknownasabileductdiverticulum. Accountfor3%ofallbileductcysts. Saccularoutpouchings,representingatruediverticulum, arisingfromthesupraduodenalextrahepaticbileductortheintrahepaticbileducts. TypeIIIAlsoknownasacholedochocele:accountfor5%ofallbileductcystsrepresentprotrusionofafocallydilated,intramuralsegmentofthedistalcommonbileductintotheduodenumCholedochocelesmaybesuccessfullymanagedwithendoscopicsphincterotomy,surgicalexcision,orboth,insymptomaticpatients.TypeIVMultiplecommunicatingintra-andextrahepaticductcysts:secondmostcommontypeofbileductcysts(10%)subdividedintosubtypes:type4a:fusiformdilationoftheentireextrahepaticbileductwithextensionofdilationoftheintrahepaticbileductstype4b:multiplecysticdilationsinvolvingonlytheextrahepaticbileductTypeVAlsoknownasCarolidisease,whichisarareformofcongenitalbiliarycysticdiseasemanifestedbycysticdilationsofintrahepaticbileducts. Associationwithbenignrenaltubularectasiaandotherformsofrenalcysticdisease.HistoryandetymologyTheToda

A, B. Coronal reformatted CT scans show cystic dilatation of common bile duct with segmental dilatation of proximal intrahepatic duct and abrupt ...NCBISkiptomaincontentSkiptonavigationResourcesHowToAboutNCBIAccesskeysMyNCBISignintoNCBISignOutTryoutPMCLabsandtelluswhatyouthink.LearnMore.JournalListKoreanJRadiolv.10(1);Jan-Feb2009PMC2647175KoreanJRadiol.2009Jan-Feb;10(1):71–80.Publishedonline2009Feb5.doi: 10.3348/kjr.2009.10.1.71PMCID:PMC2647175PMID:19182506ImagingFeaturesofAdultCholedochalCysts:aPictorialReviewHaeKyungLee,MD,1SeongJinPark,MD,1BumHaYi,MD,1ALeumLee,MD,1JongHoMoon,MD,2andYunWooChang,MD3HaeKyungLee1DepartmentofRadiology,CollegeofMedicine,SoonchunhyangUniversityBucheonHospital,Gyunggi-do420-021,Korea.FindarticlesbyHaeKyungLeeSeongJinPark1DepartmentofRadiology,CollegeofMedicine,SoonchunhyangUniversityBucheonHospital,Gyunggi-do420-021,Korea.FindarticlesbySeongJinParkBumHaYi1DepartmentofRadiology,CollegeofMedicine,SoonchunhyangUniversityBucheonHospital,Gyunggi-do420-021,Korea.FindarticlesbyBumHaYiALeumLee1DepartmentofRadiology,CollegeofMedicine,SoonchunhyangUniversityBucheonHospital,Gyunggi-do420-021,Korea.FindarticlesbyALeumLeeJongHoMoon2DepartmentofGastroenterology,CollegeofMedicine,SoonchunhyangUniversityBucheonHospital,Gyunggi-do420-021,Korea.FindarticlesbyJongHoMoonYunWooChang3DepartmentofRadiology,CollegeofMedicine,SoonchunhyangUniversitySeoulHospital,Seoul140-743,Korea.FindarticlesbyYunWooChangAuthorinformationArticlenotesCopyrightandLicenseinformationDisclaimer1DepartmentofRadiology,CollegeofMedicine,SoonchunhyangUniversityBucheonHospital,Gyunggi-do420-021,Korea.2DepartmentofGastroenterology,CollegeofMedicine,SoonchunhyangUniversityBucheonHospital,Gyunggi-do420-021,Korea.3DepartmentofRadiology,CollegeofMedicine,SoonchunhyangUniversitySeoulHospital,Seoul140-743,Korea.Correspondingauthor.Addressreprintrequeststo:HaeKyungLee,MD,DepartmentofRadiology,SoonchunhyangUniversityBucheonHospital,1174Jung-dong,Wonmi-gu,Bucheon,Gyunggi-do420-021,Korea.Tel.(8232)

RadiologyKeyFastestRadiologyInsightEngineHomeLogInCategoriesA-KBREASTIMAGINGCARDIOVASCULARIMAGINGCOMPUTERIZEDTOMOGRAPHYEMERGENCYRADIOLOGYFETALMEDICINEFRCRREADINGLISTGASTROINTESTINALIMAGINGGENERALRADIOLOGYGENITOURINARYIMAGINGHEAD&NECKIMAGINGINTERVENTIONALRADIOLOGYL-ZMAGNETICRESONANCEIMAGINGMUSCULOSKELETALIMAGINGNEUROLOGICALIMAGINGNUCLEARMEDICINEOBSTETRICS&GYNAECOLOGYIMAGINGPEDIATRICIMAGINGRADIOGRAPHICANATOMYRESPIRATORYIMAGINGULTRASONOGRAPHYMoreReferencesAbdominalKeyAnesthesiaKeyBasicmedicalKeyOtolaryngology&OphthalmologyMusculoskeletalKeyNeupsyKeyNurseKeyObstetric,GynecologyandPediatricOncology&HematologyPlasticSurgery&DermatologyClinicalDentistryRadiologyKeyThoracicKeyVeterinaryMedicineAboutContactGoldMemberMenuCholedochalCyst Diagnosisrequiresexcludingothercausesofbiliarydilatation,includingtumor,stone,orstricture Commonlyassociatedwithcholelithiasis,cystolithiasis,choledocholithiasis,andhepatolithiasis• Classifiedinto5types basedonTodaniclassification TypeI:Fusiform/cysticdilationofextrahepaticduct TypeII:TruediverticulumofsupraduodenalED TypeIII:DilationlimitedtointraduodenalsegmentofED(a.k.a.choledochocele),withdilatedsegmentofductlocatedwithinduodenalwall TypeIV:Presenceofmultiplebiliarycysts,atleast1ofwhichmustinvolveextrahepaticbileduct TypeV:Singleormultipleintrahepaticbiliarycysts,withmultipleintrahepaticcystsknownasCarolidiseasePATHOLOGY• EtiologymayberelatedtoanomalouspancreaticobiliaryjunctionorcongenitalductalplatemalformationCLINICALISSUES• Mostcommoninfemalepatients,oftenofAsiandescent• Usuallydiagnosedininfancyandchildhood• Classictriadofsymptoms:RecurrentRUQpain,jaundice,andpalpablemass• Complications:Stones,cholangitis,pancreatitis,ormalignantdegeneration(cholangiocarcinomaorgallbladdercancer)• Treatmentvariesdependingontypeofcholedochalcyst,buttypeIandIVcyststypicallyundergosurgicalexcisionandreconstructionbyRoux-en-Yhepaticojejunostomy(Left)ThisgraphicshowstheTodaniclassificationofcholedochalcysts.NotethattypeIisfusiformdilationoftheextrahepaticd

Choledochal Malformations: Surgical Implications of Radiologic Findings ... Keywords: biliary tract, Caroli disease, choledochal cysts, choledochocele, liver,​ ...AnErrorOccurredSettingYourUserCookieThissiteusescookiestoimproveperformance.Ifyourbrowserdoesnotacceptcookies,youcannotviewthissite.SettingYourBrowsertoAcceptCookiesTherearemanyreasonswhyacookiecouldnotbesetcorrectly.Belowarethemostcommonreasons:Youhavecookiesdisabledinyourbrowser.Youneedtoresetyourbrowsertoacceptcookiesortoaskyouifyouwanttoacceptcookies.Yourbrowserasksyouwhetheryouwanttoacceptcookiesandyoudeclined.Toacceptcookiesfromthissite,usetheBackbuttonandacceptthecookie.Yourbrowserdoesnotsupportcookies.Tryadifferentbrowserifyoususpectthis.Thedateonyourcomputerisinthepast.Ifyourcomputer'sclockshowsadatebefore1Jan1970,thebrowserwillautomaticallyforgetthecookie.Tofixthis,setthecorrecttimeanddateonyourcomputer.Youhaveinstalledanapplicationthatmonitorsorblockscookiesfrombeingset.Youmustdisabletheapplicationwhilelogginginorcheckwithyoursystemadministrator.WhyDoesthisSiteRequireCookies?Thissiteusescookiestoimproveperformancebyrememberingthatyouareloggedinwhenyougofrompagetopage.Toprovideaccesswithoutcookieswouldrequirethesitetocreateanewsessionforeverypageyouvisit,whichslowsthesystemdowntoanunacceptablelevel.WhatGetsStoredinaCookie?ThissitestoresnothingotherthananautomaticallygeneratedsessionIDinthecookie;nootherinformationiscaptured.Ingeneral,onlytheinformationthatyouprovide,orthechoicesyoumakewhilevisitingawebsite,canbestoredinacookie.Forexample,thesitecannotdetermineyouremailnameunlessyouchoosetotypeit.Allowingawebsitetocreateacookiedoesnotgivethatoranyothersiteaccesstotherestofyourcomputer,andonlythesitethatcreatedthecookiecanreadit.

NCBISkiptomaincontentSkiptonavigationResourcesHowToAboutNCBIAccesskeysMyNCBISignintoNCBISignOutTryoutPMCLabsandtelluswhatyouthink.LearnMore.JournalListCanJSurgv.52(6);2009DecPMC2792398CanJSurg.2009Dec;52(6):506–511.PMCID:PMC2792398PMID:20011188Language:English|FrenchCholedochalcystsPart2of3:DiagnosisJanakieSingham,MD,EricM.Yoshida,MD,andCharlesH.Scudamore,MDAuthorinformationArticlenotesCopyrightandLicenseinformationDisclaimerFromtheDepartmentsofMedicineandSurgery,theUniversityofBritishColumbia,Vancouver,BCCorrespondenceto:Dr.C.H.Scudamore,DepartmentofSurgery,UniversityofBritishColumbia,GordonandLeslieDiamondHealthCare,Centre,2775LaurelSt.,floor5,VancouverBCV5Z1M9,fax604875-5869,[email protected]©2009CanadianMedicalAssociationThisarticlehasbeencitedbyotherarticlesinPMC.Muchabouttheetiology,pathophysiology,naturalcourseandoptimaltreatmentofcysticdiseaseofthebiliarytreeremainsunderdebate.Gastroenterologists,surgeonsandradiologistsalikestillstrivetooptimizetheirrolesinthemanagementofcholedochalcysts.Tothatend,muchhasbeenwrittenaboutthisdiseaseentity,andthepurposeofthis3-partreviewistoorganizetheavailableliteratureandpresentthevarioustheoriescurrentlyarguedbytheexperts.Inpart2,weexplorethedetailssurroundingdiagnosis,describingthepresentationandimagingofthedisease.Dansunelargemesure,l’étiologie,lapathophysiologie,lecoursnatureletletraitementoptimaldelamaladiekystiquedel’arbrebiliairecontinuentdefairel’objetdedébats.Lesgastroentérologues,leschirurgiensetlesradiologuescherchenttoujoursàoptimiserleurrôlerespectifdanslapriseenchargedeskystesducholédoque.C’estpourquoileschercheursontbeaucoupécritàproposdecetteentitémorbide,etleprésentexamenen3partiesapourobjetd’organiserlesétudespubliéesetdeprésenterlesdiversesthéoriesquefontactuellementvaloirlesexperts.Dansladeuxièmepartie,nousexaminonslesdétailsentourantlediagnostic,endécrivantlaprésentationetl’imageriedelamaladie.Choledochalcysts(CCs),whicharecyststhatcanoccuranywherealongthebiliarytree,can