MainMenuforPhones...WhatisSarcoma?WhatistheInitiative?SharingtheJourneySarcomaResearchTeamSarcomaESUN  AboutUs|Liddy'sStory     EnglishDeutschEspañolFrançaisItalianoPolskiPortuguês中国的日本語Others...       MainMenuLearnAboutSarcomaWhatisSarcoma?>WhatisEpithelioidSarcoma?>>YoungAdultCancerCare1.EncouragingGuidelines2.TheSarcomaUniverse3.SarcomaCenters4.SarcomaTreatment5.ClinicalTrialsforSarcomaSharingtheJourneySarcomaResearchTeamSarcoma!ESUN:AnOnlinePeriodicalBeASuperhero!AndrewwasdiagnosedwithEpithelioidSarcomawhenhewas8yearsold.Andrew'sbrother,BenjamindecidedtoraisemoneyforresearchinAndrew'shonor.HeandhisfamilyandfriendsinWaco,Texas,organizedthe"BeaHero5k"forthreeyearsandraised$30,000forsarcomaresearch.TheFacesofEpithelioidSarcomaHide ShowMaria,30yearsoldMaria,30yearsoldCarol,59yearsoldCarol,59yearsoldAngela,24yearsoldAngela,24yearsoldKate,37yearsoldKate,37yearsoldThesephotoscomefromaroundtheworld.Learnmore.TogetherWeAreStrongEpithelioidsarcomaisoneofmorethan50kindsofsarcoma.Eachkindisrare,yetalltogethersarcomasaffecthundredsofthousandsofpeoplearoundtheworld.EpithelioidSarcomaStories,Support&ResearchIntroductionPrepare.Communicate.FindSupport.ReadourComprehensiveGuidefortheNewlyDiagnosedEpithelioidsarcomaisararesofttissuesarcomainyoungadults(20-39yearolds)involvingtheupperextremities60%ofthetime.ThenamewasgivenbyEnzingerin1970toagroupofsofttissuesarcomasthatwereconfusedwithavarietyofmalignantandbenignconditions,especiallygranulomatousprocess,synovialsarcomaandulceratingsquamouscellcarcinoma.1Thereisa"proximaltype"variantfirstdescribedin1997(seesidebarinHistologysection).Thisarticlewillfocusonconventional"distal"epithelioidsarcoma.Epithelioidsarcomaisaslowgrowingtumorwithahighrateofrecurrenceandmetastasis.Slowgrowthofthetumor,paucityofsymptoms,benignappearanceinearlystageimagingstudies,andindistinctivepathologicfindingsinsomecasesmakesthediagnosisofepithelioidsarcomachallenging.Therarityofthediseasealsomakesperforminglargecontrolledclinicaltrialstoevaluatedifferenttreat