Abstract. Hypoplastic right heart syndrome is a rare cyanotic congenital heart disease with under-development of the right ventricle, tricuspid, and ...NCBISkiptomaincontentSkiptonavigationResourcesHowToAboutNCBIAccesskeysMyNCBISignintoNCBISignOutJournalListIndianHeartJv.68(Suppl2);2016SepPMC5067759IndianHeartJ.2016Sep;68(Suppl2):S229–S232.Publishedonline2016Apr15.doi: 10.1016/j.ihj.2016.03.030PMCID:PMC5067759PMID:27751299Hypoplasticrightheartsyndrome,absentpulmonaryvalve,andnon-compactedleftventricleinanadultJagdishC.Mohan,⁎VishwasMohan,MadhuShukla,andArvindSethiAuthorinformationArticlenotesCopyrightandLicenseinformationDisclaimerDepartmentofCardiacSciences,FortisHospital,ShalimarBagh,Delhi88,IndiaJagdishC.Mohan:moc.liamg@sahkzuah15a⁎Correspondingauthor.moc.liamg@sahkzuah15aReceived2015Sep4;Accepted2016Mar22.Copyright©2016CardiologicalSocietyofIndia.PublishedbyElsevierB.V.ThisisanopenaccessarticleundertheCCBY-NC-NDlicense(http://creativecommons.org/licenses/by-nc-nd/4.0/).ThisarticlehasbeencitedbyotherarticlesinPMC.AssociatedDataSupplementaryMaterialsmmc1.jpg(201K)GUID: EF8387F2-BC17-4526-85C8-1E8792C60980mmc2.jpg(146K)GUID: B415E0F8-2F80-4FF8-BD1B-D3E73CECE5D5mmc3.jpg(155K)GUID: A367A713-DE84-48F5-AF41-7B38ABF664BFHypoplasticrightheartsyndromeisararecyanoticcongenitalheartdiseasewithunder-developmentoftherightventricle,tricuspid,andpulmonaryvalvesleadingtoright-to-leftshuntingofthebloodthroughinter-atrialseptaldefect.Perinatalmortalityishighwithveryfewpatientssurvivingtoadulthoodwithoutcorrectivesurgery.Thisreportdescribesa26-year-oldyoungwoman,whohadrecurrentabortionsandstillbirthsanddetectedtohavemarkedcyanosiswithhypoplasticrightheart,sub-arterialventricularseptaldefect,absentpulmonaryvalve,non-compactionoftheleftventricle,andbicuspidaorticvalvewithaorticregurgitation.Thepatientdiedowingtoprogressiveheartfailure4yearsafterthediagnosiswasmade.Keywords:Hypoplasticrightheartsyndrome,Absentpulmonaryvalve,Bicuspidaorticvalve,Non-compactionoftheleftventricleHypoplast