In most cases, there is no cure for HLHS; however, surgical palliation, also referred to as staged reconstruction, can be undertaken in a series of ...ForYouNews&PerspectiveDrugs&DiseasesCME&EducationAcademyVideoDecisionPointEdition:ENGLISHDEUTSCHESPAÑOLFRANÇAISPORTUGUÊSLogInSignUpIt'sFree!Edition:ENGLISHDEUTSCHESPAÑOLFRANÇAISPORTUGUÊSRegisterLogInNoResultsNoResultsForYouNews&PerspectiveDrugs&DiseasesCME&EducationAcademyVideoDecisionPointclosePleaseconfirmthatyouwouldliketologoutofMedscape.Ifyoulogout,youwillberequiredtoenteryourusernameandpasswordthenexttimeyouvisit.LogoutCancelhttps://profreg.medscape.com/px/getpracticeprofile.do?method=getProfessionalProfile&urlCache=aHR0cHM6Ly9lbWVkaWNpbmUubWVkc2NhcGUuY29tL2FydGljbGUvOTA0MTM3LW92ZXJ2aWV3processing....Drugs&Diseases>Pediatrics:CardiacDiseaseandCriticalCareMedicineSurgicalTreatmentofPediatricHypoplasticLeftHeartSyndromeUpdated:Dec20,2020Author:Ming-SingSi,MD;ChiefEditor:StuartBerger,MD more...ShareEmailPrintFeedbackCloseFacebookTwitterLinkedInGoogle+SectionsSurgicalTreatmentofPediatricHypoplasticLeftHeartSyndromeSectionsSurgicalTreatmentofPediatricHypoplasticLeftHeartSyndromeOverviewBackgroundHistoryoftheProcedurePathophysiologyEtiologyPresentationIndicationsRelevantAnatomyContraindicationsShowAllWorkupLaboratoryStudiesImagingStudiesOtherTestsDiagnosticProceduresShowAllTreatmentMedicalTherapySurgicalTherapyIntraoperativeDetailsPostoperativeDetailsFollow-upComplicationsOutcomeandPrognosisFutureandControversiesShowAllMediaGalleryReferencesOverviewBackgroundHypoplasticleftheartsyndrome(HLHS)isaspectrumofcongenitalheartdefectsthatischaracterizedbyhypoplasiaoftheleftventricleandmultilevelobstructionofsystemiccardiacoutputfromthelevelofthemitralvalvetotheproximaldescendingthoracicaorta.Othercloselyrelatedfunctionalsinglerightventriclelesionsincludedouble-outletrightventriclewithmitralatresiaandunbalancedatrioventricularseptaldefect.AcommonphysiologyofHLHSisthatthesystemiccirculationisdrivenbytherightventricleviaapatentd