The cystic hygroma (also called 'cystic lymphangioma' and 'lymphangioma cysticum') is a 'macrocytic' lymphatic malformation, and is composed of large ...DermNetprovidesGoogleTranslate,afreemachinetranslationservice.NotethatthismaynotprovideanexacttranslationinalllanguagesHOMETOPICSA-ZIMAGESCONTACTABOUTDERMDIAGBROWSEGLOSSARYQUIZZESDONATEHomearrow-right-small-blueTopicsA–Zarrow-right-small-blueLymphaticmalformationPrintLymphaticmalformationAuthor:VanessaNgan,StaffWriter,2003.UpdatedbyDrAmandaOakley,2004.Lymphaticmalformation—codesandconceptsopenCategories:Vasculardisorder,Developmentaldisorder,TumourSubcategories:Cystichygroma,Cysticlymphangioma,Lymphangiomacysticum,Cavernouslymphangioma,Lymphangiomacircumscriptum,Vascularnaevus,BirthmarkICD-10:Q89.9,D18.1ICD-11:LA90.1Z,LA90.10,LA90.11,LA90.12,LA90.1YSNOMEDCT:234095009,399882002,254793001,238799002Whatisalymphaticmalformation?Alymphaticmalformationisatypeofvascularnaevusorbirthmark duetomalformedanddilatedlymphaticvessels.Lymphaticmalformationlymphangiomacircumscriptum2lymphangiomacircumscriptum3Whatisthecauseoflymphaticmalformation?Thecauseofthemalformeddilatedlymphaticvesselsisnotfullyunderstood.Embryoniclymphsacshavenotconnectedcorrectlywiththelymphaticsystemforsomereason.Theyarenon-cancerous.Whogetslymphaticmalformation?Noparticularraceorsexismoreatrisk. Whataretheclinicalfeaturesoflymphaticmalformation?Lymphaticmalformationsarealwayspresentatbirth,althoughtheymaybemissed;theytendtobecomemoreobviousduringinfancyandchildhood.Theymayvaryinsizefromasmalldottooccasionallyinvolvingawholelimb.Althoughlymphisaclearfluid,lymphaticmalformationsoftenappearredorbluebecauseoftheinvolvementofadjacentbloodvessels.ClassificationoflymphaticmalformationTherearethreemaintypesoflymphaticmalformation:CystichygromaCavernouslymphangiomaLymphangiomacircumscriptumCystichygromaThecystichygroma(alsocalled‘cysticlymphangioma’and‘lymphangiomacysticum’)isa‘macrocytic’lymphaticmalformation,andiscomposedoflargefluid-filledspaces.Itappearsasaski